Juvenile trabecular ossifying fibroma: A case of extensive lesion of the maxilla

Abstract

Introduction and importance

Juvenile trabecular ossifying fibroma is a rare benign tumor of childhood affecting the facial bones rarely described in literature. Its aggressive growth and high tendency of recurrence make it a real challenge for diagnosis and care.

Case presentation

This article presents a case of an extensive juvenile trabecular ossifying fibroma of the maxilla in a 14-year-old boy, which required surgical intervention with immediate bone reconstruction using an autogenous graft (iliac crest).

No recurrence has been found after two and a half years of follow-up.

Clinical discussion

Common symptoms of juvenile trabecular ossifying fibroma include painless swelling, facial asymmetry, jaw deformity and teeth displacement. Differential diagnosis should consider other forms like psammomatoid ossifying fibroma, osteofibrous dysplasia, fibrous dysplasia, ameloblastoma, odontoma, or even poorly differentiated carcinoma.

Conclusion

Currently, there is no recommendation or consensus for the treatment of juvenile trabecular ossifying fibroma. The objective of treatment is also to preserve growth and development and conserve the nervous structure and the function, as mastication, vision.

Early diagnosis and appropriate care are essential to prevent morphological and functional defects in young patients. Regular and long-term follow-up is essential due to the high recurrence rate.

Highlight

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  This case report present a rare benign tumor of childhood affecting the facial bones with aggressive growth with aesthetic and functional sequelae.

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  This pathology, which is rarely found in the literature, requires rapid treatment and regular follow-up because recurrences are frequent.

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  The purpose of this article is to expose a case of extensive trabecular juvenile ossifying fibroma of the maxilla in a 14 years old boy that required surgical intervention with bone reconstruction and which we were able to survey for two and a half years.