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      Estenosis Tricuspídea Severa secundaria a enfermedad carcinoide cardiaca: presentación de caso clínico y revisión de la literatura

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          Abstract

          RESUMEN: La estenosis tricuspídea (ET) es una valvulopatía infrecuente cuyas principales etiologías son la enfermedad reumática y la endocarditis infecciosa. En raras ocasiones puede deberse a un fenómeno carcinoide subyacente, en lo que se conoce como la enfermedad carcinoide cardiaca (ECC). Esta condición lleva a la fibrosis del endocardio del ventriculo derecho, principalmente de sus válvulas, lo cual puede provocar falla cardiaca derecha, complicando el pronóstico. En este artículo se presenta un caso de una ET severa por una posible ECC, en conjunto con las imagenes ecocardiográficas obtenidas durante el abordaje diagnóstico (imágenes bidimensionales, imagen multiplanar y ecocardiografía en 3D). Se discuten las implicaciones clínicas, los retos diagnósticos, las opciones terapeuticas y el pronóstico de esta rara entidad.

          Translated abstract

          ABSTRACT Severe Tricuspid Stenosis Secondary to Cardiac Carcinoid Disease: Case Report and Literature Review Tricuspid stenosis is an unfrequent valvulopathy that can be caused by multiple etiologies, including rheumatic disease and infectious endocarditis. In rare occasions, it occurs in the context of a carcinoid syndrome, in what is known as carcinoid heart disease. This condition causes fibrosis of the valves and the endocardium of the right ventricule, which can progress into right ventricular failure, worsening the patient's prognosis. In this article, we present a case of a severe tricuspid stenosis in which this ethiology is suspected. We show the echocardiographic images obtained for the diagnosis (two-dimensional imaging, multimodal imaging and 3D echocardiography), and we discuss the clinical and diagnostic implications, therapeutic options and prognosis of this rare condition.

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          Most cited references20

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          Echocardiographic assessment of valve stenosis: EAE/ASE recommendations for clinical practice.

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            2021 ESC/EACTS Guidelines for the management of valvular heart disease: Developed by the Task Force for the management of valvular heart disease of the European Society of Cardiology (ESC) and the European Association for Cardio-Thoracic Surgery (EACTS).

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              Carcinoid heart disease.

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                Author and article information

                Journal
                rcc
                Revista Costarricense de Cardiología
                Rev. costarric. cardiol
                Asociación Costarricense de Cardiología (San José, San José, Costa Rica )
                1409-4142
                December 2023
                : 25
                : 2
                : 37-44
                Affiliations
                [3] orgnameUniversidad de Costa Rica Costa Rica
                [2] orgnameUniversidad de Costa Rica Costa Rica
                [1] San José orgnameHospital Rafael Ángel Calderón Guardia Costa Rica
                Article
                S1409-41422023000200037 S1409-4142(23)02500200037
                d3bb5d75-711e-495b-8f39-a0d80ba61d73

                This work is licensed under a Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International License.

                History
                : 17 July 2023
                : 17 November 2023
                Page count
                Figures: 0, Tables: 0, Equations: 0, References: 20, Pages: 8
                Product

                SciELO Costa Rica

                Categories
                Trabajo Original

                falla cardiaca derecha,carcinoid syndrome,right cardiac failure,Estenosis tricuspídea,síndrome carcinoide,Tricuspid stenosis

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